产品
编 号:F409831
分子式:C6H10O4
分子量:146.14
产品类型
结构图
CAS No: 626-51-7
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生物活性:
3-Methylglutaric acid, a leucine metabolite, is a conspicuous C6 dicarboxylic organic acid classically associated with two distinct leucine pathway enzyme deficiencies, 3-hydroxy-3-methylglutaryl CoA lyase (HMGCL) and 3-methylglutaconyl CoA hydratase (AUH).